Uterus, MLH1-deficient endometrioid carcinoma, MLH1 stain

Details
Disease Category
Gender
Organ System/Discipline
Diagnosis
MLH1-deficient endometrioid carcinoma
Clinical History

This section is an MLH1 immunohistochemical stain of an endometrioid carcinoma of the uterus, taken at the time of total abdominal hysterectomy (with bilateral salping-oophorectomy).

Case Discussion

Immunohistochemical staining is used to detect abnormalities in mismatch repair, which may reflect microsatellite instability. This pathway is important in Lynch Syndrome: a major cause of hereditary endometrial and colon cancers. In this case, the patient's endometrial carcinoma shows a deficiency in MLH1. This can be caused by either germline mutation of the MLH1 gene (a marker of Lynch Syndrome), or somatic hypermethylation of the gene promoter, leading to loss of expression. Therefore, immunohistochemistry alone cannot confirm Lynch Syndrome in this setting.

Image Contributors
Colgan, T., Nanji, S., Chang, M.

Cite

Colgan, T., Nanji, S., Chang, M. Uterus, MLH1-deficient endometrioid carcinoma, MLH1 stain. Digital Laboratory Medicine Library, Dept of Laboratory Medicine & Pathobiology, University of Toronto. Published . Accessed December 17, 2025. https://dev.dlml.cflabs.ca/image/uterus-mlh1-deficient-endometrioid-carcinoma-mlh1-stain-lmp23844